Sistema de entrenamiento adaptado para un joven con distrofia muscular congénita:

Daniel Josué Kirby Gómez

doi:10.46642/efd.v31i338.8401

Daniel Josué Kirby Gómez Human Performance Studio HPS.KC S.A.S.® https://linktr.ee/hps_info_ecu https://orcid.org/0009-0004-1979-5314

DOI: https://doi.org/10.46642/efd.v31i338.8401

Abstract

Congenital Muscular Dystrophy (CMD) is a hereditary neuromuscular disorder that, from birth, significantly limits motor function and overall well-being. The overall objective is to analyze the impact of an Adapted Training System (ATS), based on Therapeutic Physical Culture (TPC) and structured periodization, on the functional capacity, muscle strength, and quality of life of a young woman with CMS in Guayaquil, Ecuador, over a 24-week period. A qualitative approach was implemented using a case study design, combining the review of clinical records, semi-structured interviews, validated psychometric tests, and systematic observation. The rehabilitation program, divided into three progressive stages, emphasized biomechanical protection, personalized effort management, and the generalization of skills to the daily environment. The findings reflected substantial progress in physical independence, emotional management, and self-perception of achievements, accompanied by a reduction in psychosocial barriers. The consolidation of self-confidence and the support of the immediate family emerged as essential pillars for the continuity of the therapeutic process. Consequently, it was established that a biopsychosocial strategy, adapted to environments with material constraints, transforms the experience of patients with DMC.

Keywords: Muscular dystrophies, Exercice therapy, Therapeutic exercice, Neuromuscular rehabilitation

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Author Biography

Daniel Josué Kirby Gómez,

I have a strong background in planning, guiding, executing, and supervising individual or group physical activity programs, considering the requirements or needs of the subject in accordance with the requirements and populations served; evaluating, providing feedback, and controlling through constant monitoring and inspection the correct execution of the various exercises, the impact on individuals, and expected physical changes according to previously established objectives. I can also propose improvements or adjustments to the program or routine based on the subject's response and performance, ensuring the well-being, safety, and health of the individuals. I am trained to generate projects in physical activity using administrative and management tools. I consider myself highly technical and pride myself on being an individual of integrity, able to collaborate with teams by creating spaces for reflection and learning according to established goals.

Founder and Director of Human Performance Studio HPS.KC S.A.S.®, a company that offers training programs with national and international certification, 100% theoretical and practical. Our certifications are high-impact programs focused on providing each student with the knowledge and competencies necessary to achieve a high professional level and incorporate world-class tools.